Arrhythmogenic Left Ventricular Cardiomyopathy: Suspected by Cardiac Magnetic Resonance Imaging, Confirmed by Identification of a Novel Plakophilin-2 Variant.
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چکیده
منابع مشابه
Cardiac magnetic resonance imaging in pediatric patients ≤ 18 years with suspected arrhythmogenic right ventricular cardiomyopathy (ARVC): a correlation to genetics
Background Arrhythmogenic right ventricular cardiomyopathy (ARVC) is associated with increased risk of sudden cardiac death. It is a progressive disease that can already manifest itself during childhood and adolescence. Since little is known about the early stage in pediatric patients, this study sought to determine the influence of right and left ventricular findings from cardiac magnetic reso...
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Introduction: The correlation between right and left ventricular ejection fractions (RVEF and LVEF, respectively) has been studied in only a small number of patients with a marked decrease in RVEF and LVEF. The aim of the present study was to compare LVEF and RVEF in patients with ischemic heart disease. RVEF and LVEF were measured by Cardiovascular Magnetic Resonance (CMR) imaging. Materials a...
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Arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D) is a cardiac muscle disorder characterized pathologically by fibrofatty replacement of the right ventricular (RV) myocardium [1]. In the early stage of the disease, structural changes may be confined to, the so called "triangle of dysplasia" in the RV. Clinical expression ranges from an asymptomatic phenotype, arrhythmias or eve...
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Mitochondria play an important role in energy production for the cell. The proper function of a myocardial cell largely depends on the functional capacity of the mitochondria. Therefore it is necessary to establish a novel and reliable method for a non-invasive assessment of mitochondrial function and metabolism in humans. Although originally designed for evaluating myocardial perfusion, 99mTc...
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Magnetic Resonance Imaging (MRI) is currently considered as the noninvasive modality of choice for evaluation of patients with suspected Arrhythmogenic Right Ventricular Dysplasia (i.e., right ventricular dysplasia). As arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D) it is included in the WHO classification of cardiomyopathies. It has the unique ability to provide tissue char...
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عنوان ژورنال:
- Circulation
دوره 132 6 شماره
صفحات -
تاریخ انتشار 2015